Idiopathic pulmonary fibrosis

Drug Safety Update

 November 2020: Pirfenidone (Esbriet): risk of serious liver injury; updated advice on liver function testing

 July 2020: Systemically administered VEGF pathway inhibitors: risk of aneurysm and artery dissection

NICE guidance (see drug-specific links below)

CG163: Idiopathic pulmonary fibrosis in adults: diagnosis and management, June 2013 (last updated May 2017)

These drugs are available from specialist centres only and should be initiated and supervised by an appropriate specialist

  • On Formulary Preferred
  • On Formulary Second Line
  • On Formulary Third Line
  • Specialist Initiation
  • Secondary Care Only
  • Not Approved for Formulary